A 12-year-old girl presented with inguinal swelling and recurrent groin pain since menarche. Ultrasound showed an inguinally located ovary with normal perfusion. Herniorrhaphy revealed an ectopic inguinal left ovary with fallopian tube and atretic hemiuterus and a closed internal inguinal ring. Laparoscopy revealed a right-sided hemiuterus and vaginally palpable cervix, leading to the diagnosis of ectopic OHVIRA syndrome type 1.2. The left hemiuterus was resected and the left ovary was pulled through the inguinal canal into the abdomen. During 12 months of follow-up, the left ovary showed normal perfusion and sonomorphologic appearance, menstrual periods were uneventful.

V.E. and S.W. conceptualized the manuscript, reviewed the literature, analyzed data, and made major contribution to the writing of the manuscript. S.W., L.R., A.H.S., F.K., V.E., A.M. performed the clinical examination, surgical treatment, and clinical follow-up. V.E., S.W., and F.K. performed final review and editing of the of the manuscript. All authors have read and approved the final version of the manuscript.

Written consent for the publication of this case report was obtained from the patient. Approval for case report by the institutional ethics committee is not required.

Written informed consent for the publication of this case report and for the accompanying images was obtained from the patient and her parents.

Received: 11 June 2024

Accepted: 24 March 2025

Article published online:
08 May 2025

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